The information on benign retroperitoneal tumors is limited. Observation of a well-defined fat plane between the mass and the displaced kidney helps to confirm the extrarenal location of the mass. The aorta and inferior vena cava vessels are located within the space as well as part of the esophagus and rectum. TREATMENT OF PRIMARY AND RECURRENT KETROPERITONEAL LIPOSARCOMA ... For the management of retroperitoneal liposarcoma, complete excision of the tumor en bloc with adjacent involved organs when- ever feasible should be carried out. Adjacent, adherent, invaded: a spectrum of biologic aggressiveness rather than a rationale for selecting organ resection in surgery of primary retroperitoneal sarcomas. Primary retroperitoneal neoplasms originating outside of the solid organs are rare, but they are often malignant and can grow to a substantial size at clinical presentation. Injury to organ capsules, pleura, peritoneum, or obstruction of hollow viscera by malignancy typically produces pain and evidence of visceral dysfunction. A simple explanation of the peritoneum and classification of organs into intraperitoneal, extraperitoneal or retroperitoneal. retroperitoneal: Located outside of the peritoneum. Pathology and genetics of tumours of urinary system and male genital organs Lyon (France): IARC Press (2004) ... of post-chemotherapy retroperitoneal lymph node dissection standard recommendations in patients with testicular and primary retroperitoneal non seminomatous germ cell tumor: impact on outcome J. Clin. Patient concerns: A 41-year-old male patient presented with a chief complaint of discomfort around the waist for 2 months. Primary retroperitoneal neoplasms are a rare but diverse group of benign and malignant tumors that arise within the retroperitoneal space but outside the major organs in this space. Fairweather M, Wang J, Jo VY, et al. Inside the retroperitoneal space, there are the kidneys, adrenal glands, bladder, and ureters. Similarly, metastatic retroperitoneal lymphadenopathy and direct extension from an organ-based primary tumor are also common findings at imaging evaluation. Incidence and adverse prognostic implications of histopathologic organ invasion in primary retroperitoneal sarcoma. The organs of the gastrointestinal system include esophagus, stomach, duodenum, small intestine, large intestine, rectum and anus.The stomach is composed of different layers of cells. The majority of retroperitoneal masses arises from retroperitoneal organs and is therefore not considered primary retroperitoneal mass. The primary retroperitoneal organs are the adrenal glands, kidneys, ureter, the abdominal aorta, inferior vena cava and their branches. … Retroperitoneal structures tend to be more static than intraperitoneal ones. Although computed tomography and magnetic resonance imaging can demonstrate important characteristics of these tumors, diagnosis is often challenging for radiologists. For inoperable cases, or cases with residual disease or suspicious of residual disease following surgery, intensive radiation therapy should be … Most are malignant lesions. 2017;224:876-83. IVP demonstrates displacement of retroperitoneal organs or of gas within the lumen of retroperitoneal portions of the intestines (ascending and descending colon). Primary retroperitoneal serous cystadenomas are homogeneous, unilocular, thin-walled cystic masses. Primary retroperitoneal neoplasms are a rare group of tumors which do not arise from a specific organ but rather originate from tissues or rests of embryonic cells which exist in the retroperitoneum . Although it can affect any organ, the common forms found in adults are mesenteric and/or retroperitoneal CL. Although they are more prevalent in adults, they can occur at any age. Woodward P.J. Primary retroperitoneal tumors present a broad spectrum of pathologic entities and arise from actual tissues in the same space or from embryonic rests found therein [].Diagnosis of these tumors begins with affirmation of their retroperitoneal location and then determination of whether the lesion is primarily retroperitoneal or is arising secondarily from a retroperitoneal organ []. According to literature the primary retroperitoneal malignant pathology is rare, representing less than 0.5% of all malignancies. The full spectrum of visceral pain syndromes is not discussed here. Key Difference – Intraperitoneal vs Retroperitoneal. Visceral - forms surfaces of organs, the serosa. Primary retroperitoneal neoplasms are a rare but diverse group of benign and malignant tumors that arise within the retroperitoneal space but outside the major organs in this space. Strauss DC, Renne SL, Gronchi A. Primary retroperitoneal masses constitute a heterogeneous group of uncommon lesions and represent a challenge due to overlap-ping imaging findings. Primary retroperitoneal neoplasms are a rare but an important group of neoplasms. If they grow large enough, they tend to compress and deform adjacent organs, giving clinicians a misimpression of malignant pattern of behavior. Most primary retroperitoneal neoplasms develop from the mesodermal system. The primary retroperitoneal tumors form a rare and diverse group of neoplasms, the origin of which is independent of the various retroperitoneal organs and unrelated to systemic diseases, such as lymphomas, lymphadenopathy, or metastases. Primary tumors of the retroperitoneum develop independently from cells distinct from the major retroperitoneal organs such as the kidneys, adrenal glands, pancreas, colon and duodenum, and major blood vessels. PRIMARY RETROPERITONEAL EXTRA-ORGAN TUMORS (PRET) - SURGICAL TACTICS. Key Terms. https://www.wisegeek.com/what-are-retroperitoneal-organs.htm Primary retroperitoneal mature cystic teratomas are exceedingly uncommon in males aged 50 years and above, and only seven cases have been reported in the literature so far. Retroperitoneal sarcoma is an orphan malignant disease with a low incidence. The most common variety is sarcoma, which accounts for up to 90 % of lesions after lymphoma is excluded. A primary retroperitoneal tumor is generally considered to be one that originates independently within the retroperitoneal space without primary anatomic connection to any of the retroperitoneal organs. Parietal - covers the abdominal wall. Primary retroperitoneal cavernous hemangioma (PRCH) in an adult is extremely rare. Primary retroperitoneal tumors are relatively rare entities, presenting a variety of benign or malignant histological features. 21. [Article in Bulgarian, English] Sokolov M, Velev G, Maslyankov S, Toshev S, Angelov K, Gribnev P, Vasileva M, Khayat N, Todorov G. INTRODUCTION: Retroperitoneal tumors, in general, are rare tumors which histopathological characteristics and biological behavior can be considered as benign or malignant. Organs are retroperitoneal if they have peritoneum on their anterior side only. Approach to retroperitoneal masses. Patients and Methods A total of 382 patients with primary RPS were analyzed. Its discovery in adults is rare. They usually occur in infants less than 6 months and young females. The peritoneum is the serous membrane that forms the thin lining of the abdomen. Approximately 70–80% of primary retroperitoneal soft‐tissue tumors are malignant; however, these only account for 0.1–0.2% of all malignancies. The peritoneum has visceral and parietal layers, just like the pleural cavity. 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